ICD-10-CM › E

ICD-10-CM codes starting with E

1,270 codes, page 10 of 13. Every code ever valid for billing is listed, including those now retired.

CodeDescriptionStatus
E70.33 Albinism with hematologic abnormality Not billable
E70.330 Chediak-Higashi syndrome Valid
E70.331 Hermansky-Pudlak syndrome Valid
E70.338 Other albinism with hematologic abnormality Valid
E70.339 Albinism with hematologic abnormality, unspecified Valid
E70.39 Other specified albinism Valid
E70.4 Disorders of histidine metabolism Not billable
E70.40 Disorders of histidine metabolism, unspecified Valid
E70.41 Histidinemia Valid
E70.49 Other disorders of histidine metabolism Valid
E70.5 Disorders of tryptophan metabolism Valid
E70.8 Other disorders of aromatic amino-acid metabolism Not billable
E70.81 Aromatic L-amino acid decarboxylase deficiency Valid
E70.89 Other disorders of aromatic amino-acid metabolism Valid
E70.9 Disorder of aromatic amino-acid metabolism, unspecified Valid
E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Not billable
E71.0 Maple-syrup-urine disease Valid
E71.1 Other disorders of branched-chain amino-acid metabolism Not billable
E71.11 Branched-chain organic acidurias Not billable
E71.110 Isovaleric acidemia Valid
E71.111 3-methylglutaconic aciduria Valid
E71.118 Other branched-chain organic acidurias Valid
E71.12 Disorders of propionate metabolism Not billable
E71.120 Methylmalonic acidemia Valid
E71.121 Propionic acidemia Valid
E71.128 Other disorders of propionate metabolism Valid
E71.19 Other disorders of branched-chain amino-acid metabolism Valid
E71.2 Disorder of branched-chain amino-acid metabolism, unspecified Valid
E71.3 Disorders of fatty-acid metabolism Not billable
E71.30 Disorder of fatty-acid metabolism, unspecified Valid
E71.31 Disorders of fatty-acid oxidation Not billable
E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency Valid
E71.311 Medium chain acyl CoA dehydrogenase deficiency Valid
E71.312 Short chain acyl CoA dehydrogenase deficiency Valid
E71.313 Glutaric aciduria type II Valid
E71.314 Muscle carnitine palmitoyltransferase deficiency Valid
E71.318 Other disorders of fatty-acid oxidation Valid
E71.32 Disorders of ketone metabolism Valid
E71.39 Other disorders of fatty-acid metabolism Valid
E71.4 Disorders of carnitine metabolism Not billable
E71.40 Disorder of carnitine metabolism, unspecified Valid
E71.41 Primary carnitine deficiency Valid
E71.42 Carnitine deficiency due to inborn errors of metabolism Valid
E71.43 Iatrogenic carnitine deficiency Valid
E71.44 Other secondary carnitine deficiency Not billable
E71.440 Ruvalcaba-Myhre-Smith syndrome Valid
E71.448 Other secondary carnitine deficiency Valid
E71.5 Peroxisomal disorders Not billable
E71.50 Peroxisomal disorder, unspecified Valid
E71.51 Disorders of peroxisome biogenesis Not billable
E71.510 Zellweger syndrome Valid
E71.511 Neonatal adrenoleukodystrophy Valid
E71.518 Other disorders of peroxisome biogenesis Valid
E71.52 X-linked adrenoleukodystrophy Not billable
E71.520 Childhood cerebral X-linked adrenoleukodystrophy Valid
E71.521 Adolescent X-linked adrenoleukodystrophy Valid
E71.522 Adrenomyeloneuropathy Valid
E71.528 Other X-linked adrenoleukodystrophy Valid
E71.529 X-linked adrenoleukodystrophy, unspecified type Valid
E71.53 Other group 2 peroxisomal disorders Valid
E71.54 Other peroxisomal disorders Not billable
E71.540 Rhizomelic chondrodysplasia punctata Valid
E71.541 Zellweger-like syndrome Valid
E71.542 Other group 3 peroxisomal disorders Valid
E71.548 Other peroxisomal disorders Valid
E72 Other disorders of amino-acid metabolism Not billable
E72.0 Disorders of amino-acid transport Not billable
E72.00 Disorders of amino-acid transport, unspecified Valid
E72.01 Cystinuria Valid
E72.02 Hartnup's disease Valid
E72.03 Lowe's syndrome Valid
E72.04 Cystinosis Valid
E72.09 Other disorders of amino-acid transport Valid
E72.1 Disorders of sulfur-bearing amino-acid metabolism Not billable
E72.10 Disorders of sulfur-bearing amino-acid metabolism, unspecified Valid
E72.11 Homocystinuria Valid
E72.12 Methylenetetrahydrofolate reductase deficiency Valid
E72.19 Other disorders of sulfur-bearing amino-acid metabolism Valid
E72.2 Disorders of urea cycle metabolism Not billable
E72.20 Disorder of urea cycle metabolism, unspecified Valid
E72.21 Argininemia Valid
E72.22 Arginosuccinic aciduria Valid
E72.23 Citrullinemia Valid
E72.29 Other disorders of urea cycle metabolism Valid
E72.3 Disorders of lysine and hydroxylysine metabolism Valid
E72.4 Disorders of ornithine metabolism Valid
E72.5 Disorders of glycine metabolism Not billable
E72.50 Disorder of glycine metabolism, unspecified Valid
E72.51 Non-ketotic hyperglycinemia Valid
E72.52 Trimethylaminuria Valid
E72.53 Primary hyperoxaluria Not billable
E72.530 Primary hyperoxaluria, type 1 Valid
E72.538 Other specified primary hyperoxaluria Valid
E72.539 Primary hyperoxaluria, unspecified Valid
E72.54 Secondary hyperoxaluria Not billable
E72.540 Dietary hyperoxaluria Valid
E72.541 Enteric hyperoxaluria Valid
E72.548 Other secondary hyperoxaluria Valid
E72.549 Secondary hyperoxaluria, unspecified Valid
E72.59 Other disorders of glycine metabolism Valid
Page 10 of 13