ICD-10-CM › E
ICD-10-CM codes starting with E
1,270 codes, page 10 of 13. Every code ever valid for billing is listed, including those now retired.
| Code | Description | Status |
|---|---|---|
| E70.33 | Albinism with hematologic abnormality | Not billable |
| E70.330 | Chediak-Higashi syndrome | Valid |
| E70.331 | Hermansky-Pudlak syndrome | Valid |
| E70.338 | Other albinism with hematologic abnormality | Valid |
| E70.339 | Albinism with hematologic abnormality, unspecified | Valid |
| E70.39 | Other specified albinism | Valid |
| E70.4 | Disorders of histidine metabolism | Not billable |
| E70.40 | Disorders of histidine metabolism, unspecified | Valid |
| E70.41 | Histidinemia | Valid |
| E70.49 | Other disorders of histidine metabolism | Valid |
| E70.5 | Disorders of tryptophan metabolism | Valid |
| E70.8 | Other disorders of aromatic amino-acid metabolism | Not billable |
| E70.81 | Aromatic L-amino acid decarboxylase deficiency | Valid |
| E70.89 | Other disorders of aromatic amino-acid metabolism | Valid |
| E70.9 | Disorder of aromatic amino-acid metabolism, unspecified | Valid |
| E71 | Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism | Not billable |
| E71.0 | Maple-syrup-urine disease | Valid |
| E71.1 | Other disorders of branched-chain amino-acid metabolism | Not billable |
| E71.11 | Branched-chain organic acidurias | Not billable |
| E71.110 | Isovaleric acidemia | Valid |
| E71.111 | 3-methylglutaconic aciduria | Valid |
| E71.118 | Other branched-chain organic acidurias | Valid |
| E71.12 | Disorders of propionate metabolism | Not billable |
| E71.120 | Methylmalonic acidemia | Valid |
| E71.121 | Propionic acidemia | Valid |
| E71.128 | Other disorders of propionate metabolism | Valid |
| E71.19 | Other disorders of branched-chain amino-acid metabolism | Valid |
| E71.2 | Disorder of branched-chain amino-acid metabolism, unspecified | Valid |
| E71.3 | Disorders of fatty-acid metabolism | Not billable |
| E71.30 | Disorder of fatty-acid metabolism, unspecified | Valid |
| E71.31 | Disorders of fatty-acid oxidation | Not billable |
| E71.310 | Long chain/very long chain acyl CoA dehydrogenase deficiency | Valid |
| E71.311 | Medium chain acyl CoA dehydrogenase deficiency | Valid |
| E71.312 | Short chain acyl CoA dehydrogenase deficiency | Valid |
| E71.313 | Glutaric aciduria type II | Valid |
| E71.314 | Muscle carnitine palmitoyltransferase deficiency | Valid |
| E71.318 | Other disorders of fatty-acid oxidation | Valid |
| E71.32 | Disorders of ketone metabolism | Valid |
| E71.39 | Other disorders of fatty-acid metabolism | Valid |
| E71.4 | Disorders of carnitine metabolism | Not billable |
| E71.40 | Disorder of carnitine metabolism, unspecified | Valid |
| E71.41 | Primary carnitine deficiency | Valid |
| E71.42 | Carnitine deficiency due to inborn errors of metabolism | Valid |
| E71.43 | Iatrogenic carnitine deficiency | Valid |
| E71.44 | Other secondary carnitine deficiency | Not billable |
| E71.440 | Ruvalcaba-Myhre-Smith syndrome | Valid |
| E71.448 | Other secondary carnitine deficiency | Valid |
| E71.5 | Peroxisomal disorders | Not billable |
| E71.50 | Peroxisomal disorder, unspecified | Valid |
| E71.51 | Disorders of peroxisome biogenesis | Not billable |
| E71.510 | Zellweger syndrome | Valid |
| E71.511 | Neonatal adrenoleukodystrophy | Valid |
| E71.518 | Other disorders of peroxisome biogenesis | Valid |
| E71.52 | X-linked adrenoleukodystrophy | Not billable |
| E71.520 | Childhood cerebral X-linked adrenoleukodystrophy | Valid |
| E71.521 | Adolescent X-linked adrenoleukodystrophy | Valid |
| E71.522 | Adrenomyeloneuropathy | Valid |
| E71.528 | Other X-linked adrenoleukodystrophy | Valid |
| E71.529 | X-linked adrenoleukodystrophy, unspecified type | Valid |
| E71.53 | Other group 2 peroxisomal disorders | Valid |
| E71.54 | Other peroxisomal disorders | Not billable |
| E71.540 | Rhizomelic chondrodysplasia punctata | Valid |
| E71.541 | Zellweger-like syndrome | Valid |
| E71.542 | Other group 3 peroxisomal disorders | Valid |
| E71.548 | Other peroxisomal disorders | Valid |
| E72 | Other disorders of amino-acid metabolism | Not billable |
| E72.0 | Disorders of amino-acid transport | Not billable |
| E72.00 | Disorders of amino-acid transport, unspecified | Valid |
| E72.01 | Cystinuria | Valid |
| E72.02 | Hartnup's disease | Valid |
| E72.03 | Lowe's syndrome | Valid |
| E72.04 | Cystinosis | Valid |
| E72.09 | Other disorders of amino-acid transport | Valid |
| E72.1 | Disorders of sulfur-bearing amino-acid metabolism | Not billable |
| E72.10 | Disorders of sulfur-bearing amino-acid metabolism, unspecified | Valid |
| E72.11 | Homocystinuria | Valid |
| E72.12 | Methylenetetrahydrofolate reductase deficiency | Valid |
| E72.19 | Other disorders of sulfur-bearing amino-acid metabolism | Valid |
| E72.2 | Disorders of urea cycle metabolism | Not billable |
| E72.20 | Disorder of urea cycle metabolism, unspecified | Valid |
| E72.21 | Argininemia | Valid |
| E72.22 | Arginosuccinic aciduria | Valid |
| E72.23 | Citrullinemia | Valid |
| E72.29 | Other disorders of urea cycle metabolism | Valid |
| E72.3 | Disorders of lysine and hydroxylysine metabolism | Valid |
| E72.4 | Disorders of ornithine metabolism | Valid |
| E72.5 | Disorders of glycine metabolism | Not billable |
| E72.50 | Disorder of glycine metabolism, unspecified | Valid |
| E72.51 | Non-ketotic hyperglycinemia | Valid |
| E72.52 | Trimethylaminuria | Valid |
| E72.53 | Primary hyperoxaluria | Not billable |
| E72.530 | Primary hyperoxaluria, type 1 | Valid |
| E72.538 | Other specified primary hyperoxaluria | Valid |
| E72.539 | Primary hyperoxaluria, unspecified | Valid |
| E72.54 | Secondary hyperoxaluria | Not billable |
| E72.540 | Dietary hyperoxaluria | Valid |
| E72.541 | Enteric hyperoxaluria | Valid |
| E72.548 | Other secondary hyperoxaluria | Valid |
| E72.549 | Secondary hyperoxaluria, unspecified | Valid |
| E72.59 | Other disorders of glycine metabolism | Valid |