ICD-10-CM › E00-E89 › E70-E88 › E71.31 Disorders of fatty-acid oxidation › E71.313

E71.313

Glutaric aciduria type II

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

  1. FY2007 Added to the draft code set draft Glutaric aciduria type II

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

  • Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Codes in the same group

CodeDescriptionStatus
E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency Valid
E71.311 Medium chain acyl CoA dehydrogenase deficiency Valid
E71.312 Short chain acyl CoA dehydrogenase deficiency Valid
E71.314 Muscle carnitine palmitoyltransferase deficiency Valid
E71.318 Other disorders of fatty-acid oxidation Valid