ICD-10-CM › E00-E89 › E70-E88 › E72.53 Primary hyperoxaluria › E72.538

E72.538

Other specified primary hyperoxaluria

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2026 onwards.

What has happened to this code

Every change the publisher made, from 2026 to now.

  1. FY2026 Added to the code set Other specified primary hyperoxaluria

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E72 Other disorders of amino-acid metabolism

Excludes1 - never coded here

  • disorders of:
  • aromatic amino-acid metabolism (E70.-)
  • branched-chain amino-acid metabolism (E71.0-E71.2)
  • fatty-acid metabolism (E71.3)
  • purine and pyrimidine metabolism (E79.-)
  • gout (M1A.-, M10.-)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

  • Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Codes in the same group

CodeDescriptionStatus
E72.530 Primary hyperoxaluria, type 1 Valid
E72.539 Primary hyperoxaluria, unspecified Valid