Other disorders of branched-chain amino-acid metabolism

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 3 more specific codes instead:

E71.11 Branched-chain organic acidurias (also a header)
E71.12 Disorders of propionate metabolism (also a header)
E71.19 Other disorders of branched-chain amino-acid metabolism

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2012 Added to the draft code set draft Other disorders of branched-chain amino-acid metabolism

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

Codes in the same group

Code	Description	Status
E71.0	Maple-syrup-urine disease	Valid
E71.2	Disorder of branched-chain amino-acid metabolism, unspecified	Valid
E71.3	Disorders of fatty-acid metabolism	Not billable
E71.4	Disorders of carnitine metabolism	Not billable
E71.5	Peroxisomal disorders	Not billable