Long chain/very long chain acyl CoA dehydrogenase deficiency

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Long chain/very long chain acyl CoA dehydrogenase deficiency

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Deficit
Avitaminosis
Hypovitaminosis
Vitamin deficiency
Leukoencephalopathy
Deprivation > vitamins
Deficiency, deficient > factor
Defect, defective > coagulation
Deficiency, deficient > clotting
Disturbance > absorption > vitamin
Encephalopathy > in > lack of vitamin
Deficiency, deficient > clotting factor NEC
Deficiency, deficient > coagulation NOS > clotting factor NEC
Deficiency, deficient > LCAD
Deficiency, deficient > VLCAD
Disorder > fatty acid > oxidation > LCAD
Deficiency, deficient > dehydrogenase > long chain/very long chain acyl CoA

Codes in the same group

Code	Description	Status
E71.311	Medium chain acyl CoA dehydrogenase deficiency	Valid
E71.312	Short chain acyl CoA dehydrogenase deficiency	Valid
E71.313	Glutaric aciduria type II	Valid
E71.314	Muscle carnitine palmitoyltransferase deficiency	Valid
E71.318	Other disorders of fatty-acid oxidation	Valid