Other disorders of urea cycle metabolism

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Other disorders of urea cycle metabolism

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E72 Other disorders of amino-acid metabolism

Excludes1 - never coded here

disorders of:
aromatic amino-acid metabolism (E70.-)
branched-chain amino-acid metabolism (E71.0-E71.2)
fatty-acid metabolism (E71.3)
purine and pyrimidine metabolism (E79.-)
gout (M1A.-, M10.-)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Urea > cycle metabolism disorder
Disorder > urea cycle metabolism > other specified

Codes in the same group

Code	Description	Status
E72.20	Disorder of urea cycle metabolism, unspecified	Valid
E72.21	Argininemia	Valid
E72.22	Arginosuccinic aciduria	Valid
E72.23	Citrullinemia	Valid