ICD-10-CM › E

ICD-10-CM codes starting with E

1,270 codes, page 11 of 13. Every code ever valid for billing is listed, including those now retired.

CodeDescriptionStatus
E72.8 Other specified disorders of amino-acid metabolism Not billable
E72.81 Disorders of gamma aminobutyric acid metabolism Valid
E72.89 Other specified disorders of amino-acid metabolism Valid
E72.9 Disorder of amino-acid metabolism, unspecified Valid
E73 Lactose intolerance Not billable
E73.0 Congenital lactase deficiency Valid
E73.1 Secondary lactase deficiency Valid
E73.8 Other lactose intolerance Valid
E73.9 Lactose intolerance, unspecified Valid
E74 Other disorders of carbohydrate metabolism Not billable
E74.0 Glycogen storage disease Not billable
E74.00 Glycogen storage disease, unspecified Valid
E74.01 von Gierke disease Valid
E74.02 Pompe disease Valid
E74.03 Cori disease Valid
E74.04 McArdle disease Valid
E74.05 Lysosome-associated membrane protein 2 [LAMP2] deficiency Valid
E74.09 Other glycogen storage disease Valid
E74.1 Disorders of fructose metabolism Not billable
E74.10 Disorder of fructose metabolism, unspecified Valid
E74.11 Essential fructosuria Valid
E74.12 Hereditary fructose intolerance Valid
E74.19 Other disorders of fructose metabolism Valid
E74.2 Disorders of galactose metabolism Not billable
E74.20 Disorders of galactose metabolism, unspecified Valid
E74.21 Galactosemia Valid
E74.29 Other disorders of galactose metabolism Valid
E74.3 Other disorders of intestinal carbohydrate absorption Not billable
E74.31 Sucrase-isomaltase deficiency Valid
E74.39 Other disorders of intestinal carbohydrate absorption Valid
E74.4 Disorders of pyruvate metabolism and gluconeogenesis Valid
E74.8 Other specified disorders of carbohydrate metabolism Not billable
E74.81 Disorders of glucose transport, not elsewhere classified Not billable
E74.810 Glucose transporter protein type 1 deficiency Valid
E74.818 Other disorders of glucose transport Valid
E74.819 Disorders of glucose transport, unspecified Valid
E74.82 Disorders of citrate metabolism Not billable
E74.820 SLC13A5 Citrate Transporter Disorder Valid
E74.829 Other disorders of citrate metabolism Valid
E74.89 Other specified disorders of carbohydrate metabolism Valid
E74.9 Disorder of carbohydrate metabolism, unspecified Valid
E75 Disorders of sphingolipid metabolism and other lipid storage disorders Not billable
E75.0 GM2 gangliosidosis Not billable
E75.00 GM2 gangliosidosis, unspecified Valid
E75.01 Sandhoff disease Valid
E75.02 Tay-Sachs disease Valid
E75.09 Other GM2 gangliosidosis Valid
E75.1 Other and unspecified gangliosidosis Not billable
E75.10 Unspecified gangliosidosis Valid
E75.11 Mucolipidosis IV Valid
E75.19 Other gangliosidosis Valid
E75.2 Other sphingolipidosis Not billable
E75.21 Fabry (-Anderson) disease Valid
E75.22 Gaucher disease Valid
E75.23 Krabbe disease Valid
E75.24 Niemann-Pick disease Not billable
E75.240 Niemann-Pick disease type A Valid
E75.241 Niemann-Pick disease type B Valid
E75.242 Niemann-Pick disease type C Valid
E75.243 Niemann-Pick disease type D Valid
E75.244 Niemann-Pick disease type A/B Valid
E75.248 Other Niemann-Pick disease Valid
E75.249 Niemann-Pick disease, unspecified Valid
E75.25 Metachromatic leukodystrophy Valid
E75.26 Sulfatase deficiency Valid
E75.27 Pelizaeus-Merzbacher disease Valid
E75.28 Canavan disease Valid
E75.29 Other sphingolipidosis Valid
E75.3 Sphingolipidosis, unspecified Valid
E75.4 Neuronal ceroid lipofuscinosis Valid
E75.5 Other lipid storage disorders Valid
E75.6 Lipid storage disorder, unspecified Valid
E76 Disorders of glycosaminoglycan metabolism Not billable
E76.0 Mucopolysaccharidosis, type I Not billable
E76.01 Hurler's syndrome Valid
E76.02 Hurler-Scheie syndrome Valid
E76.03 Scheie's syndrome Valid
E76.1 Mucopolysaccharidosis, type II Valid
E76.2 Other mucopolysaccharidoses Not billable
E76.21 Morquio mucopolysaccharidoses Not billable
E76.210 Morquio A mucopolysaccharidoses Valid
E76.211 Morquio B mucopolysaccharidoses Valid
E76.219 Morquio mucopolysaccharidoses, unspecified Valid
E76.22 Sanfilippo mucopolysaccharidoses Valid
E76.29 Other mucopolysaccharidoses Valid
E76.3 Mucopolysaccharidosis, unspecified Valid
E76.8 Other disorders of glucosaminoglycan metabolism Valid
E76.9 Glucosaminoglycan metabolism disorder, unspecified Valid
E77 Disorders of glycoprotein metabolism Not billable
E77.0 Defects in post-translational modification of lysosomal enzymes Valid
E77.1 Defects in glycoprotein degradation Valid
E77.8 Other disorders of glycoprotein metabolism Valid
E77.9 Disorder of glycoprotein metabolism, unspecified Valid
E78 Disorders of lipoprotein metabolism and other lipidemias Not billable
E78.0 Pure hypercholesterolemia Not billable
E78.00 Pure hypercholesterolemia, unspecified Valid
E78.01 Familial hypercholesterolemia Not billable
E78.010 Homozygous familial hypercholesterolemia [HoFH] Valid
E78.011 Heterozygous familial hypercholesterolemia [HeFH] Valid
E78.019 Familial hypercholesterolemia, unspecified Valid
Page 11 of 13