Disorder of branched-chain amino-acid metabolism, unspecified

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Disorder of branched-chain amino-acid metabolism, unspecified

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Disorder > amino-acid > metabolism
Branched-chain amino-acid disorder
Disorder > branched-chain amino-acid metabolism
Disturbance > metabolism > amino-acid > branched-chain
Disorder > metabolism NOS > amino-acid > branched chain

Codes in the same group

Code	Description	Status
E71.0	Maple-syrup-urine disease	Valid
E71.1	Other disorders of branched-chain amino-acid metabolism	Not billable
E71.3	Disorders of fatty-acid metabolism	Not billable
E71.4	Disorders of carnitine metabolism	Not billable
E71.5	Peroxisomal disorders	Not billable