ICD-10-CM › E00-E89 › E70-E88 › E75.2 Other sphingolipidosis › E75.26

Valid for claims with a date of service in the current code year.

Valid FY2019 onwards.

What has happened to this code

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E75 Disorders of sphingolipid metabolism and other lipid storage disorders

Excludes1 - never coded here

• mucolipidosis, types I-III (E77.0-E77.1)
• Refsum's disease (G60.1)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

• androgen insensitivity syndrome (E34.5-)
• congenital adrenal hyperplasia (E25.0)
• hemolytic anemias attributable to enzyme disorders (D55.-)
• Marfan syndrome (Q87.4-)
• 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

• Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

• Deficit
• Avitaminosis
• Hypovitaminosis
• Vitamin deficiency
• Leukoencephalopathy
• Deprivation > vitamins
• Deficiency, deficient > factor
• Defect, defective > coagulation
• Deficiency, deficient > clotting
• Disturbance > absorption > vitamin
• Encephalopathy > in > lack of vitamin
• Deficiency, deficient > clotting factor NEC
• Deficiency, deficient > coagulation NOS > clotting factor NEC
• MSD
• Deficiency, deficient > sulfatase
• Deficiency, deficient > multiple sulfatase

Codes in the same group

Code	Description	Status
E75.21	Fabry (-Anderson) disease	Valid
E75.22	Gaucher disease	Valid
E75.23	Krabbe disease	Valid
E75.24	Niemann-Pick disease	Not billable
E75.25	Metachromatic leukodystrophy	Valid
E75.27	Pelizaeus-Merzbacher disease	Valid
E75.28	Canavan disease	Valid
E75.29	Other sphingolipidosis	Valid