von Gierke disease

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Von Gierke's disease
FY2010 Draft description revised draft ~~Von Gierke's disease~~ von Gierke disease

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E74 Other disorders of carbohydrate metabolism

Excludes1 - never coded here

diabetes mellitus (E08-E13)
hypoglycemia NOS (E16.2)
increased secretion of glucagon (E16.3)
mucopolysaccharidosis (E76.0-E76.3)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Deficit
Avitaminosis
Glycogenosis
Hypovitaminosis
Vitamin deficiency
Leukoencephalopathy
Deprivation > vitamins
Glycogen > infiltration
Thesaurismosis, glycogen
Glycogen > storage disease
Deficiency, deficient > factor
Defect, defective > coagulation
Deficiency, deficient > clotting
Disturbance > absorption > vitamin
Encephalopathy > in > lack of vitamin
Disease, diseased > storage > glycogen
Deficiency, deficient > clotting factor NEC
Infiltrate, infiltration > liver > glycogen
Infiltrate, infiltration > glycogen, glycogenic
Deficiency, deficient > coagulation NOS > clotting factor NEC
Gierke's disease
Von Gierke's disease
Disease, diseased > Gierke's
Van Creveld-von Gierke disease
Disease, diseased > von Gierke's
Disease, diseased > van Creveld-von Gierke
Deficiency, deficient > glucose-6-phosphatase
Disease, diseased > glycogen storage > type I
Disease, diseased > glycogen storage > Von Gierke's
Disease, diseased > glycogen storage > glucose-6-phosphatase deficiency

Codes in the same group

Code	Description	Status
E74.00	Glycogen storage disease, unspecified	Valid
E74.02	Pompe disease	Valid
E74.03	Cori disease	Valid
E74.04	McArdle disease	Valid
E74.05	Lysosome-associated membrane protein 2 [LAMP2] deficiency	Valid
E74.09	Other glycogen storage disease	Valid