ICD-10-CM › E00-E89 › E70-E88 › E75 Disorders of sphingolipid... › E75.6
Lipid storage disorder, unspecified
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.
- FY2007 Added to the draft code set draft Lipid storage disorder, unspecified
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from E75 Disorders of sphingolipid metabolism and other lipid storage disorders
Excludes1 - never coded here
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
Inherited from the E70-E88 section Metabolic disorders (E70-E88)
Excludes1 - never coded here
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
Excludes2 - not included here
- Ehlers-Danlos syndromes (Q79.6-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Lipoidosis
- Behr's disease
- Stargardt's disease
- Macula > degeneration
- Retinitis > disciformis
- Kuhnt-Junius degeneration
- Heredodegeneration, macular
- Disease, diseased > cerebral
- Disorder > retina > dystrophy
- Sclerosis, sclerotic > choroid
- Disorder > retina > retinopathy
- Disorder > retina > degeneration
- Disorder > choroid > degeneration
- Macula > degeneration > hereditary
- Retinopathy > pigmentary, congenital
- Detachment > retina > pigment epithelium
- Disorder > retina > macular degeneration
- Degeneration, degenerative > eye, macular
- Degeneration, degenerative > Kuhnt-Junius
- Degeneration, degenerative > chorioretinal
- Degeneration, degenerative > tapetoretinal
- Disease, diseased > cerebellar, cerebellum
- Degeneration, degenerative > retina > macula
- Degeneration, degenerative > Bruch's membrane
- Degeneration, degenerative > retina > hereditary
- Degeneration, degenerative > retina > pigmentary
- Degeneration, degenerative > choroid > hereditary
- Degeneration, degenerative > retina > Kuhnt-Junius
- Degeneration, degenerative > retina > posterior pole
- Degeneration, degenerative > eye, macular > congenital or hereditary
- Degeneration, degenerative > macula, macular > congenital or hereditary
- Lipidosis
- Hyperlipidosis
- Disorder > lipid > storage
- Disease, diseased > lipid-storage
- Myopathy > in > lipid storage disease
- Dystrophy, dystrophia > retinal > in > systemic lipidoses
- Dystrophy, dystrophia > retinal > in > lipid storage disorders
- Degeneration, degenerative > brain > in > lipidosis > generalized
Codes in the same group
| Code | Description | Status |
|---|---|---|
| E75.0 | GM2 gangliosidosis | Not billable |
| E75.1 | Other and unspecified gangliosidosis | Not billable |
| E75.2 | Other sphingolipidosis | Not billable |
| E75.3 | Sphingolipidosis, unspecified | Valid |
| E75.4 | Neuronal ceroid lipofuscinosis | Valid |
| E75.5 | Other lipid storage disorders | Valid |