ICD-10-CM › E00-E89 › E70-E88 › E codes › E75

E75

Disorders of sphingolipid metabolism and other lipid storage disorders

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 7 more specific codes instead:

  • E75.0 GM2 gangliosidosis (also a header)
  • E75.1 Other and unspecified gangliosidosis (also a header)
  • E75.2 Other sphingolipidosis (also a header)
  • E75.3 Sphingolipidosis, unspecified
  • E75.4 Neuronal ceroid lipofuscinosis
  • E75.5 Other lipid storage disorders
  • E75.6 Lipid storage disorder, unspecified

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

  1. FY2012 Added to the draft code set draft Disorders of sphingolipid metabolism and other lipid storage disorders

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

This code

Excludes1 - never coded here

  • mucolipidosis, types I-III (E77.0-E77.1)
  • Refsum's disease (G60.1)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

  • Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.