ICD-10-CM › E00-E89 › E70-E88 › E76 Disorders of glycosaminoglycan metabolism › E76.0
E76.0
Mucopolysaccharidosis, type I
Not billableICD-10-CM diagnosis code.
This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.
Submit one of these 3 more specific codes instead:
What has happened to this code
Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.
- FY2012 Added to the draft code set draft Mucopolysaccharidosis, type I
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from the E70-E88 section Metabolic disorders (E70-E88)
Excludes1 - never coded here
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
Excludes2 - not included here
- Ehlers-Danlos syndromes (Q79.6-)
Codes in the same group
| Code | Description | Status |
|---|---|---|
| E76.1 | Mucopolysaccharidosis, type II | Valid |
| E76.2 | Other mucopolysaccharidoses | Not billable |
| E76.3 | Mucopolysaccharidosis, unspecified | Valid |
| E76.8 | Other disorders of glucosaminoglycan metabolism | Valid |
| E76.9 | Glucosaminoglycan metabolism disorder, unspecified | Valid |