ICD-10-CM › E00-E89 › E70-E88 › E77 Disorders of glycoprotein metabolism › E77.0
Defects in post-translational modification of lysosomal enzymes
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.
- FY2007 Added to the draft code set draft Defects in post-translational modification of lysosomal enzymes
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from the E70-E88 section Metabolic disorders (E70-E88)
Excludes1 - never coded here
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
Excludes2 - not included here
- Ehlers-Danlos syndromes (Q79.6-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Mucolipidosis > II, III
- Disease, diseased > I-cell
- Polydystrophy, pseudo-Hurler
- Pseudo-Hurler's polydystrophy
- Disease, diseased > pseudo-Hurler's
- Defect, defective > lysosomal enzyme, post-translational modification
- Defect, defective > modification, lysosomal enzymes, post-translational
Codes in the same group
| Code | Description | Status |
|---|---|---|
| E77.1 | Defects in glycoprotein degradation | Valid |
| E77.8 | Other disorders of glycoprotein metabolism | Valid |
| E77.9 | Disorder of glycoprotein metabolism, unspecified | Valid |