ICD-10-CM › D50-D89 › D80-D89 › D81 Combined immunodeficiencies › D81.3

D81.3

Adenosine deaminase [ADA] deficiency

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

Billable FY2016 to FY2019, and a category header from FY2020.

Submit one of these 4 more specific codes instead:

  • D81.30 Adenosine deaminase deficiency, unspecified
  • D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
  • D81.32 Adenosine deaminase 2 deficiency
  • D81.39 Other adenosine deaminase deficiency

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

  1. FY2007 Added to the draft code set draft Adenosine deaminase [ADA] deficiency
  2. FY2020 Stopped being billable

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from D81 Combined immunodeficiencies

Excludes1 - never coded here

  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Inherited from the D80-D89 section Certain disorders involving the immune mechanism (D80-D89)

Excludes1 - never coded here

  • autoimmune disease (systemic) NOS (M35.9)
  • functional disorders of polymorphonuclear neutrophils (D71-)

Excludes2 - not included here

  • human immunodeficiency virus [HIV] disease (B20)

Includes

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Codes in the same group

CodeDescriptionStatus
D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis Valid
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers Valid
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers Valid
D81.4 Nezelof's syndrome Valid
D81.5 Purine nucleoside phosphorylase [PNP] deficiency Valid
D81.6 Major histocompatibility complex class I deficiency Valid
D81.7 Major histocompatibility complex class II deficiency Valid
D81.8 Other combined immunodeficiencies Not billable
D81.9 Combined immunodeficiency, unspecified Valid