Severe combined immunodeficiency due to adenosine deaminase deficiency

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2020 onwards.

What has happened to this code

Every change the publisher made, from 2020 to now.

FY2020 Added to the code set Severe combined immunodeficiency due to adenosine deaminase deficiency

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from D81 Combined immunodeficiencies

Excludes1 - never coded here

autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Inherited from the D80-D89 section Certain disorders involving the immune mechanism (D80-D89)

Excludes1 - never coded here

autoimmune disease (systemic) NOS (M35.9)
functional disorders of polymorphonuclear neutrophils (D71-)

Excludes2 - not included here

human immunodeficiency virus [HIV] disease (B20)

Includes

defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Deficit
Avitaminosis
Hypovitaminosis
Vitamin deficiency
Leukoencephalopathy
Deprivation > vitamins
Deficiency, deficient > factor
Deficiency, deficient > immuno
Defect, defective > coagulation
Deficiency, deficient > clotting
Disturbance > absorption > vitamin
Encephalopathy > in > lack of vitamin
Deficiency, deficient > clotting factor NEC
Immunodeficiency > with > adenosine-deaminase deficiency
Deficiency, deficient > coagulation NOS > clotting factor NEC
Immunodeficiency > severe combined > due to adenosine deaminase deficiency
Deficiency, deficient > adenosine deaminase > with severe combined immunodeficiency

Codes in the same group

Code	Description	Status
D81.30	Adenosine deaminase deficiency, unspecified	Valid
D81.32	Adenosine deaminase 2 deficiency	Valid
D81.39	Other adenosine deaminase deficiency	Valid