ICD-10-CM › M00-M99 › M04 › M04 Autoinflammatory syndromes › M04.3
M04.3
VEXAS syndrome
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2027 to now.
- FY2027 Added to the code set VEXAS syndrome
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from M04 Autoinflammatory syndromes
Excludes2 - not included here
- Crohn's disease (K50.-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Syndrome > VEXAS
- Syndrome > vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic
Codes in the same group
| Code | Description | Status |
|---|---|---|
| M04.1 | Periodic fever syndromes | Valid |
| M04.2 | Cryopyrin-associated periodic syndromes | Valid |
| M04.8 | Other autoinflammatory syndromes | Valid |
| M04.9 | Autoinflammatory syndrome, unspecified | Valid |