ICD-10-CM › M00-M99 › M04 › M04 Autoinflammatory syndromes › M04.1
M04.1
Periodic fever syndromes
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2017 to now.
- FY2017 Added to the code set Periodic fever syndromes
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from M04 Autoinflammatory syndromes
Excludes2 - not included here
- Crohn's disease (K50.-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Deficit
- Arthropyosis
- Avitaminosis
- Pyoarthrosis
- Septic > joint
- Abscess > joint
- Febris, febrile
- Hypovitaminosis
- Vitamin deficiency
- Leukoencephalopathy
- Deprivation > vitamins
- Pyemia, pyemic > joint
- Pyarthritis, pyarthrosis
- Fever > viral hemorrhagic
- Arthritis, arthritic > septic
- Deficiency, deficient > factor
- Arthritis, arthritic > purulent
- Defect, defective > coagulation
- Deficiency, deficient > clotting
- Suppuration, suppurative > joint
- Arthritis, arthritic > suppurative
- Disturbance > absorption > vitamin
- Arthritis, arthritic > in > infection
- Encephalopathy > in > lack of vitamin
- Disease, diseased > joint > suppurative
- Polyarthritis, polyarthropathy > infective
- Deficiency, deficient > clotting factor NEC
- Arthritis, arthritic > in > coliform bacilli
- Arthritis, arthritic > infectious or infective
- Deficiency, deficient > coagulation NOS > clotting factor NEC
- TRAPS
- Fever > periodic
- Syndrome > periodic fever
- Fever > Mediterranean > familial
- Mediterranean > fever > familial
- Syndrome > hyperimmunoglobulin D
- Deficiency, deficient > mevalonate kinase
- Arthritis, arthritic > in > Mediterranean fever, familial
- Syndrome > tumor necrosis factor receptor associated periodic
Codes in the same group
| Code | Description | Status |
|---|---|---|
| M04.2 | Cryopyrin-associated periodic syndromes | Valid |
| M04.3 | VEXAS syndrome | Valid |
| M04.8 | Other autoinflammatory syndromes | Valid |
| M04.9 | Autoinflammatory syndrome, unspecified | Valid |