ICD-10-CM › M00-M99 › M04 › M04 Autoinflammatory syndromes › M04.2
M04.2
Cryopyrin-associated periodic syndromes
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2017 to now.
- FY2017 Added to the code set Cryopyrin-associated periodic syndromes
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from M04 Autoinflammatory syndromes
Excludes2 - not included here
- Crohn's disease (K50.-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Hives
- Wheal
- Bold hives
- Rash > nettle
- Exanthem, exanthema
- CINCA
- NOMID
- Syndrome > Muckle-Wells
- Urticaria > familial cold
- Syndrome > cryopyrin-associated periodic
- Syndrome > familial cold autoinflammatory
- Disorder > neonatal onset multisystemic inflammatory
- Syndrome > chronic > infantile neurological, cutaneous and articular
Codes in the same group
| Code | Description | Status |
|---|---|---|
| M04.1 | Periodic fever syndromes | Valid |
| M04.3 | VEXAS syndrome | Valid |
| M04.8 | Other autoinflammatory syndromes | Valid |
| M04.9 | Autoinflammatory syndrome, unspecified | Valid |