ICD-10-CM › E00-E89 › E70-E88 › E88 Other and unspecified metabolic disorders › E88.1

E88.1

Lipodystrophy, not elsewhere classified

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

Billable FY2016 to FY2025, and a category header from FY2026.

Submit one of these 6 more specific codes instead:

  • E88.10 Lipodystrophy, unspecified
  • E88.11 Partial lipodystrophy
  • E88.12 Generalized lipodystrophy
  • E88.13 Localized lipodystrophy
  • E88.14 HIV-associated lipodystrophy
  • E88.19 Other lipodystrophy, not elsewhere classified

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

  1. FY2007 Added to the draft code set draft Lipodystrophy, not elsewhere classified
  2. FY2026 Stopped being billable

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E88 Other and unspecified metabolic disorders

Excludes1 - never coded here

  • histiocytosis X (chronic) (C96.6)

Use additional code

  • codes for associated conditions

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

  • Ehlers-Danlos syndromes (Q79.6-)

Codes in the same group

CodeDescriptionStatus
E88.0 Disorders of plasma-protein metabolism, not elsewhere classified Not billable
E88.2 Lipomatosis, not elsewhere classified Valid
E88.3 Tumor lysis syndrome Valid
E88.4 Mitochondrial metabolism disorders Not billable
E88.8 Other specified metabolic disorders Not billable
E88.9 Metabolic disorder, unspecified Valid
E88.A Wasting disease (syndrome) due to underlying condition Valid