Other lipodystrophy, not elsewhere classified

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2026 onwards.

What has happened to this code

Every change the publisher made, from 2026 to now.

FY2026 Added to the code set Other lipodystrophy, not elsewhere classified

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E88 Other and unspecified metabolic disorders

Excludes1 - never coded here

histiocytosis X (chronic) (C96.6)

Use additional code

codes for associated conditions

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Syndrome > Hollander-Simons
Lipodystrophy > specified type NEC

Codes in the same group

Code	Description	Status
E88.10	Lipodystrophy, unspecified	Valid
E88.11	Partial lipodystrophy	Valid
E88.12	Generalized lipodystrophy	Valid
E88.13	Localized lipodystrophy	Valid
E88.14	HIV-associated lipodystrophy	Valid