Disorders of plasma-protein metabolism, not elsewhere classified

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 3 more specific codes instead:

E88.01 Alpha-1-antitrypsin deficiency
E88.02 Plasminogen deficiency
E88.09 Other disorders of plasma-protein metabolism, not elsewhere classified

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2012 Added to the draft code set draft Disorders of plasma-protein metabolism, not elsewhere classified

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E88 Other and unspecified metabolic disorders

Excludes1 - never coded here

histiocytosis X (chronic) (C96.6)

Use additional code

codes for associated conditions

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

Codes in the same group

Code	Description	Status
E88.1	Lipodystrophy, not elsewhere classified	Not billable
E88.2	Lipomatosis, not elsewhere classified	Valid
E88.3	Tumor lysis syndrome	Valid
E88.4	Mitochondrial metabolism disorders	Not billable
E88.8	Other specified metabolic disorders	Not billable
E88.9	Metabolic disorder, unspecified	Valid
E88.A	Wasting disease (syndrome) due to underlying condition	Valid