Biotin-dependent carboxylase deficiency

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 3 more specific codes instead:

D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2012 Added to the draft code set draft Biotin-dependent carboxylase deficiency

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from D81 Combined immunodeficiencies

Excludes1 - never coded here

autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Inherited from the D80-D89 section Certain disorders involving the immune mechanism (D80-D89)

Excludes1 - never coded here

autoimmune disease (systemic) NOS (M35.9)
functional disorders of polymorphonuclear neutrophils (D71-)

Excludes2 - not included here

human immunodeficiency virus [HIV] disease (B20)

Includes

defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis

Codes in the same group

Code	Description	Status
D81.82	Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]	Valid
D81.89	Other combined immunodeficiencies	Valid