Congenital cutaneous mastocytosis

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Mastocytosis
FY2018 Description revised ~~Mastocytosis~~ Congenital cutaneous mastocytosis

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from Q82 Other congenital malformations of skin

Excludes1 - never coded here

acrodermatitis enteropathica (E83.2)
congenital erythropoietic porphyria (E80.0)
pilonidal cyst or sinus (L05.-)
Sturge-Weber (-Dimitri) syndrome (Q85.89)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Hives
Wheal
Bold hives
Rash > nettle
Exanthem, exanthema
Urticaria > pigmentosa > congenital
Mastocytosis > cutaneous > congenital
Urticaria > pigmentosa > of newborn onset
Urticaria > pigmentosa > of neonatal onset
Mastocytosis > cutaneous > of newborn onset
Mastocytosis > cutaneous > of neonatal onset

Codes in the same group

Code	Description	Status
Q82.0	Hereditary lymphedema	Valid
Q82.1	Xeroderma pigmentosum	Valid
Q82.3	Incontinentia pigmenti	Valid
Q82.4	Ectodermal dysplasia (anhidrotic)	Valid
Q82.5	Congenital non-neoplastic nevus	Valid
Q82.6	Congenital sacral dimple	Valid
Q82.8	Other specified congenital malformations of skin	Valid
Q82.9	Congenital malformation of skin, unspecified	Valid