ICD-10-CM › Q00-QA1 › Q80-Q89 › Q82 Other congenital malformations of skin › Q82.0
Hereditary lymphedema
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.
- FY2007 Added to the draft code set draft Hereditary lymphedema
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from Q82 Other congenital malformations of skin
Excludes1 - never coded here
- acrodermatitis enteropathica (E83.2)
- congenital erythropoietic porphyria (E80.0)
- pilonidal cyst or sinus (L05.-)
- Sturge-Weber (-Dimitri) syndrome (Q85.89)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Pitted
- Pitting
- Lipedema
- Retained
- Lymphedema
- Retention > water
- Edema, edematous > lower limbs
- Edema, edematous > extremities, lower
- Trophedema
- Meige's syndrome
- Milroy's disease
- Tropholymphedema
- Meige-Milroy disease
- Nonne-Milroy syndrome
- Lymphedema > congenital
- Lymphedema > hereditary
- Elephantiasis > congenital
- Disease, diseased > Meige's
- Edema, edematous > Milroy's
- Disease, diseased > Milroy's
- Edema, edematous > hereditary
- Syndrome > Nonne-Milroy-Meige
- Pseudoelephantiasis neuroarthritica
- Edema, edematous > legs > hereditary
- Edema, edematous > chronic hereditary
- Disease, diseased > Nonne-Milroy-Meige
- Edema, edematous > familial, hereditary
Codes in the same group
| Code | Description | Status |
|---|---|---|
| Q82.1 | Xeroderma pigmentosum | Valid |
| Q82.2 | Congenital cutaneous mastocytosis | Valid |
| Q82.3 | Incontinentia pigmenti | Valid |
| Q82.4 | Ectodermal dysplasia (anhidrotic) | Valid |
| Q82.5 | Congenital non-neoplastic nevus | Valid |
| Q82.6 | Congenital sacral dimple | Valid |
| Q82.8 | Other specified congenital malformations of skin | Valid |
| Q82.9 | Congenital malformation of skin, unspecified | Valid |