ICD-10-CM › E00-E89 › E70-E88 › E88.4 Mitochondrial metabolism disorders › E88.43
E88.43
Disorders of mitochondrial tRNA synthetases
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2024 to now.
- FY2024 Added to the code set Disorders of mitochondrial tRNA synthetases
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from E88 Other and unspecified metabolic disorders
Excludes1 - never coded here
- histiocytosis X (chronic) (C96.6)
Use additional code
- codes for associated conditions
Inherited from the E70-E88 section Metabolic disorders (E70-E88)
Excludes1 - never coded here
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
Excludes2 - not included here
- Ehlers-Danlos syndromes (Q79.6-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- LBSL
- LTBL
- Disorder > metabolism NOS > mitochondrial > ARS2-related
- Disorder > metabolism NOS > mitochondrial > tRNA synthetases
- Disorder > metabolism NOS > mitochondrial > aminoacyl-tRNA synthetase
- Leukoencephalopathy > with > thalamus - brainstem involvement - high lactate
- Leukoencephalopathy > with > brainstem - spinal cord involvement - lactate elevation
Codes in the same group
| Code | Description | Status |
|---|---|---|
| E88.40 | Mitochondrial metabolism disorder, unspecified | Valid |
| E88.41 | MELAS syndrome | Valid |
| E88.42 | MERRF syndrome | Valid |
| E88.49 | Other mitochondrial metabolism disorders | Valid |