ICD-10-CM › E00-E89 › E70-E88 › E88.4 Mitochondrial metabolism disorders › E88.42
MERRF syndrome
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2010 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.
- FY2010 Added to the draft code set draft MERRF syndrome
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from E88 Other and unspecified metabolic disorders
Excludes1 - never coded here
- histiocytosis X (chronic) (C96.6)
Use additional code
- codes for associated conditions
Inherited from the E70-E88 section Metabolic disorders (E70-E88)
Excludes1 - never coded here
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
Excludes2 - not included here
- Ehlers-Danlos syndromes (Q79.6-)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- MERRF syndrome
- Syndrome > MERRF
- Disorder > metabolism NOS > mitochondrial > MERRF syndrome
Codes in the same group
| Code | Description | Status |
|---|---|---|
| E88.40 | Mitochondrial metabolism disorder, unspecified | Valid |
| E88.41 | MELAS syndrome | Valid |
| E88.43 | Disorders of mitochondrial tRNA synthetases | Valid |
| E88.49 | Other mitochondrial metabolism disorders | Valid |