ICD-10-CM › E00-E89 › E70-E88 › E83.82 Disorders of pyrophosphate metabolism › E83.820

Valid for claims with a date of service in the current code year.

Valid FY2026 onwards.

What has happened to this code

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E83 Disorders of mineral metabolism

Excludes1 - never coded here

• dietary mineral deficiency (E58-E61)
• parathyroid disorders (E20-E21)
• vitamin D deficiency (E55.-)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

• androgen insensitivity syndrome (E34.5-)
• congenital adrenal hyperplasia (E25.0)
• hemolytic anemias attributable to enzyme disorders (D55.-)
• Marfan syndrome (Q87.4-)
• 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

• Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

• IIAC
• Calcification > idiopathic infantile arterial
• Calcification > arterial > generalized, of infancy
• Calcification > arterial > generalized, of infancy > with > unspecified genetic causality

Codes in the same group

Code	Description	Status
E83.821	ENPP1 deficiency causing generalized arterial calcification of infancy	Valid
E83.822	ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2	Valid
E83.823	ABCC6 deficiency causing generalized arterial calcification of infancy	Valid
E83.824	ABCC6 deficiency causing pseudoxanthoma elasticum	Valid
E83.825	CD73 deficiency causing arterial calcification	Valid