ICD-10-CM › E00-E89 › E70-E88 › E83.8 Other disorders of mineral metabolism › E83.82

E83.82

Disorders of pyrophosphate metabolism

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2026 onwards. It has never been valid for submission on its own.

Submit one of these 6 more specific codes instead:

  • E83.820 Generalized arterial calcification of infancy with unspecified genetic causality
  • E83.821 ENPP1 deficiency causing generalized arterial calcification of infancy
  • E83.822 ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
  • E83.823 ABCC6 deficiency causing generalized arterial calcification of infancy
  • E83.824 ABCC6 deficiency causing pseudoxanthoma elasticum
  • E83.825 CD73 deficiency causing arterial calcification

What has happened to this code

Every change the publisher made, from 2026 to now.

  1. FY2026 Added to the code set Disorders of pyrophosphate metabolism

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E83 Disorders of mineral metabolism

Excludes1 - never coded here

  • dietary mineral deficiency (E58-E61)
  • parathyroid disorders (E20-E21)
  • vitamin D deficiency (E55.-)

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

  • Ehlers-Danlos syndromes (Q79.6-)

Codes in the same group

CodeDescriptionStatus
E83.81 Hungry bone syndrome Valid
E83.89 Other disorders of mineral metabolism Valid