Other disorders of bilirubin metabolism

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Other disorders of bilirubin metabolism

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E80 Disorders of porphyrin and bilirubin metabolism

Includes

defects of catalase and peroxidase

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Rotor's disease or syndrome
Disorder > bilirubin excretion
Dubin-Johnson disease or syndrome
Hyperbilirubinemia > constitutional
Hyperbilirubinemia > familial conjugated
Defect, defective > bilirubin excretion NEC
Bilirubin metabolism disorder > specified NEC
Disorder > metabolism NOS > bilirubin > specified NEC

Codes in the same group

Code	Description	Status
E80.0	Hereditary erythropoietic porphyria	Valid
E80.1	Porphyria cutanea tarda	Valid
E80.2	Other and unspecified porphyria	Not billable
E80.3	Defects of catalase and peroxidase	Valid
E80.4	Gilbert syndrome	Valid
E80.5	Crigler-Najjar syndrome	Valid
E80.7	Disorder of bilirubin metabolism, unspecified	Valid