Other and unspecified porphyria

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 3 more specific codes instead:

E80.20 Unspecified porphyria
E80.21 Acute intermittent (hepatic) porphyria
E80.29 Other porphyria

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2012 Added to the draft code set draft Other and unspecified porphyria

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E80 Disorders of porphyrin and bilirubin metabolism

Includes

defects of catalase and peroxidase

Inherited from the E70-E88 section Metabolic disorders (E70-E88)

Excludes1 - never coded here

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 - not included here

Ehlers-Danlos syndromes (Q79.6-)

Codes in the same group

Code	Description	Status
E80.0	Hereditary erythropoietic porphyria	Valid
E80.1	Porphyria cutanea tarda	Valid
E80.3	Defects of catalase and peroxidase	Valid
E80.4	Gilbert syndrome	Valid
E80.5	Crigler-Najjar syndrome	Valid
E80.6	Other disorders of bilirubin metabolism	Valid
E80.7	Disorder of bilirubin metabolism, unspecified	Valid