ICD-10-CM › Q00-QA1 › Q80-Q89 › Q89.8 Other specified congenital malformations › Q89.81

Q89.81

Kabuki syndrome

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2026 onwards.

What has happened to this code

Every change the publisher made, from 2026 to now.

  1. FY2026 Added to the code set Kabuki syndrome

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Codes in the same group

CodeDescriptionStatus
Q89.89 Other specified congenital malformations Valid