Marfan syndrome with cardiovascular manifestations

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 2 more specific codes instead:

Q87.410 Marfan syndrome with aortic dilation
Q87.418 Marfan syndrome with other cardiovascular manifestations

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2012 Added to the draft code set draft Marfan's syndrome with cardiovascular manifestations
FY2024 Description revised ~~Marfan's syndrome with cardiovascular manifestations~~ Marfan syndrome with cardiovascular manifestations

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from Q87 Other specified congenital malformation syndromes affecting multiple systems

Use additional code

code(s) to identify all associated manifestations

Codes in the same group

Code	Description	Status
Q87.40	Marfan syndrome, unspecified	Valid
Q87.42	Marfan syndrome with ocular manifestations	Valid
Q87.43	Marfan syndrome with skeletal manifestation	Valid