ICD-10-CM › Q00-QA1 › Q80-Q89 › Q85.8 Other phakomatoses, not elsewhere... › Q85.83

Q85.83

Von Hippel-Lindau syndrome

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2023 onwards.

What has happened to this code

Every change the publisher made, from 2023 to now.

  1. FY2023 Added to the code set Von Hippel-Lindau syndrome

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from Q85 Phakomatoses, not elsewhere classified

Excludes1 - never coded here

  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Codes in the same group

CodeDescriptionStatus
Q85.81 PTEN hamartoma tumor syndrome Valid
Q85.82 Other Cowden syndrome Valid
Q85.89 Other phakomatoses, not elsewhere classified Valid