ICD-10-CM › Q00-QA1 › Q00-Q07 › Q04 Other congenital malformations of brain › Q04.1
Arhinencephaly
ValidICD-10-CM diagnosis code.
Valid for claims with a date of service in the current code year.
What has happened to this code
Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.
- FY2007 Added to the draft code set draft Arhinencephaly
Official coding rules
Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.
Inherited from Q04 Other congenital malformations of brain
Excludes1 - never coded here
- cyclopia (Q87.0)
- macrocephaly (Q75.3)
How CDC's index refers to this code
Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.
- Arhinencephaly
Codes in the same group
| Code | Description | Status |
|---|---|---|
| Q04.0 | Congenital malformations of corpus callosum | Valid |
| Q04.2 | Holoprosencephaly | Valid |
| Q04.3 | Other reduction deformities of brain | Valid |
| Q04.4 | Septo-optic dysplasia of brain | Valid |
| Q04.5 | Megalencephaly | Valid |
| Q04.6 | Congenital cerebral cysts | Valid |
| Q04.8 | Other specified congenital malformations of brain | Valid |
| Q04.9 | Congenital malformation of brain, unspecified | Valid |