Nephrotic syndrome

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 12 more specific codes instead:

N04.0 Nephrotic syndrome with minor glomerular abnormality
N04.1 Nephrotic syndrome with focal and segmental glomerular lesions
N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis (also a header)
N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
N04.6 Nephrotic syndrome with dense deposit disease
N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
N04.8 Nephrotic syndrome with other morphologic changes
N04.9 Nephrotic syndrome with unspecified morphologic changes
N04.A Nephrotic syndrome with C3 glomerulonephritis
N04.B Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN) (also a header)

What has happened to this code

Every change the publisher made, from 2012 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2012 Added to the draft code set draft Nephrotic syndrome

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

This code

Includes

congenital nephrotic syndrome
lipoid nephrosis

Inherited from the N00-N08 section Glomerular diseases (N00-N08)

Excludes1 - never coded here

hypertensive chronic kidney disease (I12.-)

Code also

any associated kidney failure (N17-N19).