Progressive systemic sclerosis

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Progressive systemic sclerosis

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from M34 Systemic sclerosis [scleroderma]

Excludes1 - never coded here

circumscribed scleroderma (L94.0)
neonatal scleroderma (P83.88)

Inherited from the M30-M36 section Systemic connective tissue disorders (M30-M36)

Excludes1 - never coded here

autoimmune disease, single organ or single cell-type -code to relevant condition category

Includes

autoimmune disease NOS
collagen (vascular) disease NOS
systemic autoimmune disease
systemic collagen (vascular) disease

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Scleriasis
Dermatosclerosis
Sclerema > adultorum
Buschke's > scleredema
Scleredema > adultorum
Scleredema > Buschke's
Scleroderma, sclerodermia
Thibierge-Weissenbach syndrome
Acroscleriasis, acroscleroderma, acrosclerosis
Sclerosis, sclerotic > progressive, systemic
Sclerosis, sclerotic > systemic > progressive

Codes in the same group

Code	Description	Status
M34.1	CR(E)ST syndrome	Valid
M34.2	Systemic sclerosis induced by drug and chemical	Valid
M34.8	Other forms of systemic sclerosis	Not billable
M34.9	Systemic sclerosis, unspecified	Valid