Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2021 onwards.

What has happened to this code

Every change the publisher made, from 2021 to now.

FY2021 Added to the code set Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from G40 Epilepsy and recurrent seizures

Excludes1 - never coded here

conversion disorder with seizures (F44.5)
convulsions NOS (R56.9)
post traumatic seizures (R56.1)
seizure (convulsive) NOS (R56.9)
seizure of newborn (P90)

Excludes2 - not included here

hippocampal sclerosis (G93.81)
mesial temporal sclerosis (G93.81)
temporal sclerosis (G93.81)
Todd's paralysis (G83.84)

Note

the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

CDKL5
Disorder > Cyclin-Dependent Kinase-Like 5 Deficiency

Codes in the same group

Code	Description	Status
G40.40	Other generalized epilepsy and epileptic syndromes, not intractable	Not billable
G40.41	Other generalized epilepsy and epileptic syndromes, intractable	Not billable