Congenital adrenogenital disorders associated with enzyme deficiency

ValidICD-10-CM diagnosis code.

Valid for claims with a date of service in the current code year.

Valid FY2016 onwards.

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Congenital adrenogenital disorders associated with enzyme deficiency

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from E25 Adrenogenital disorders

Excludes1 - never coded here

indeterminate sex and pseudohermaphroditism (Q56)
chromosomal abnormalities (Q90-Q99)

Includes

adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
Female adrenal pseudohermaphroditism
Female heterosexual precocious pseudopuberty
Male isosexual precocious pseudopuberty
Male macrogenitosomia praecox
Male sexual precocity with adrenal hyperplasia
Male virilization (female)

Inherited from the E20-E35 section Disorders of other endocrine glands (E20-E35)

Excludes1 - never coded here

galactorrhea (N64.3)
gynecomastia (N62)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

Deficit
Overactive
Avitaminosis
Hypovitaminosis
Vitamin deficiency
Leukoencephalopathy
Deprivation > vitamins
Disorder > adrenogenital
Pseudohermaphroditism > male
Deficiency, deficient > factor
Pseudohermaphroditism > female
Defect, defective > coagulation
Deficiency, deficient > clotting
Disturbance > absorption > vitamin
Encephalopathy > in > lack of vitamin
Deficiency, deficient > clotting factor NEC
Deficiency, deficient > coagulation NOS > clotting factor NEC
Virilism > congenital
Virilization > congenital
Adrenogenitalism, congenital
Macrogenitosomia > congenital
Hyperadrenocorticism > congenital
Adrenogenital syndrome > salt loss
Defect, defective > 11-hydroxylase
Defect, defective > 21-hydroxylase
Adrenogenital syndrome > congenital
Deficiency, deficient > 11-hydroxylase
Deficiency, deficient > 21-hydroxylase
Pseudohermaphroditism > female > adrenal
Hyperplasia, hyperplastic > adrenal > congenital
Masculinization with adrenal hyperplasia > congenital
Defect, defective > 3-beta-hydroxysteroid dehydrogenase
Precocity, sexual > with adrenal hyperplasia > congenital
Deficiency, deficient > 3-beta hydroxysteroid dehydrogenase
Hyperplasia, hyperplastic > adrenal > congenital > salt-losing
Hyperplasia, hyperplastic > adrenal > with > virilization > congenital
Syndrome > adrenogenital > congenital, associated with enzyme deficiency
Hyperplasia, hyperplastic > adrenal > with > sexual precocity > congenital
Hyperplasia, hyperplastic > adrenal > with > virilism, adrenal > congenital
Hyperfunction > adrenal cortex, not associated with Cushing's syndrome > virilism > congenital

Codes in the same group

Code	Description	Status
E25.8	Other adrenogenital disorders	Valid
E25.9	Adrenogenital disorder, unspecified	Valid