ICD-10-CM › D50-D89 › D65-D69 › D68.0 Von Willebrand disease › D68.01

Valid for claims with a date of service in the current code year.

Valid FY2023 onwards.

What has happened to this code

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from D68 Other coagulation defects

Excludes1 - never coded here

• abnormal coagulation profile NOS (R79.1)

Excludes2 - not included here

• coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
• coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

How CDC's index refers to this code

Wording from the official alphabetic index. Much of it appears nowhere in the code description, which is why a search for the everyday phrase so often finds nothing.

• Bleeder
• Deficit
• Missing
• Amputation
• Avitaminosis
• Angiohemophilia
• Hypovitaminosis
• Pseudohemophilia
• Vitamin deficiency
• Leukoencephalopathy
• Loss > organ or part
• Hemophilia > vascular
• Syndrome > Willebrand
• Deprivation > vitamins
• Willebrand thrombopathy
• Absence > toe > with foot
• Syndrome > von Willebrand
• Thrombopathy > constitutional
• Deficiency, deficient > factor
• Defect, defective > coagulation
• Deficiency, deficient > clotting
• Thrombopathy > Willebrand-Jurgens
• Disturbance > absorption > vitamin
• Von Willebrand disease or syndrome
• Syndrome > von Willebrand > acquired
• Encephalopathy > in > lack of vitamin
• Absence > von Willebrand factor, complete
• Deficiency, deficient > clotting factor NEC
• Disease, diseased > Minot-von Willebrand-Jürgens
• Minot-von Willebrand-Jurgens disease or syndrome
• Deficiency, deficient > platelet NEC > constitutional
• Defect, defective > platelets, qualitative > constitutional
• Deficiency, deficient > factor > VIII > with vascular defect
• Deficiency, deficient > coagulation NOS > clotting factor NEC
• Deficiency, deficient > von Willebrand factor > total quantitative
• Deficiency, deficient > von Willebrand factor > partial quantitative
• Defect, defective > qualitative, of von Willebrand factor > with > hyper-adhesive forms
• Defect, defective > qualitative, of von Willebrand factor > with > markedly decreased affinity for factor VIII
• Defect, defective > qualitative, of von Willebrand factor > with > increased affinity for platelet glycoprotein lb
• Defect, defective > qualitative, of von Willebrand factor > with > high-molecular-weight von Willebrand factor loss

Showing 40 of 47 index phrases.

Codes in the same group

Code	Description	Status
D68.00	Von Willebrand disease, unspecified	Valid
D68.02	Von Willebrand disease, type 2	Not billable
D68.03	Von Willebrand disease, type 3	Valid
D68.04	Acquired von Willebrand disease	Valid
D68.09	Other von Willebrand disease	Valid