Creutzfeldt-Jakob disease

Not billableICD-10-CM diagnosis code.

This code exists but cannot be submitted on its own. It groups the more specific codes beneath it.

A category header for its whole life, FY2016 onwards. It has never been valid for submission on its own.

Submit one of these 3 more specific codes instead:

A81.00 Creutzfeldt-Jakob disease, unspecified
A81.01 Variant Creutzfeldt-Jakob disease
A81.09 Other Creutzfeldt-Jakob disease

What has happened to this code

Every change the publisher made, from 2007 to now. Entries marked draft are from the pre-implementation releases: ICD-10 took effect on 1 October 2015, so nothing before FY2016 was ever valid on a claim.

FY2007 Added to the draft code set draft Creutzfeldt-Jakob disease
FY2010 Removed from the draft draft
FY2012 Returned to the draft draft

Official coding rules

Published by CDC for FY2027. A rule attached to a category binds every code beneath it, so the rules inherited from this code's ancestors are shown with the code they come from.

Inherited from A81 Atypical virus infections of central nervous system

Use additional code

code, if applicable, to identify:
dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
mild neurocognitive disorder due to known physiological condition (F06.7-)

Includes

diseases of the central nervous system caused by prions

Inherited from the A80-A89 section Viral and prion infections of the central nervous system (A80-A89)

Excludes1 - never coded here

postpolio syndrome (G14)
sequelae of poliomyelitis (B91)
sequelae of viral encephalitis (B94.1)

Codes in the same group

Code	Description	Status
A81.1	Subacute sclerosing panencephalitis	Valid
A81.2	Progressive multifocal leukoencephalopathy	Valid
A81.8	Other atypical virus infections of central nervous system	Not billable
A81.9	Atypical virus infection of central nervous system, unspecified	Valid